P year‎ > ‎Paediatrics‎ > ‎

12.09.19 Vascular anomalies

Terminology

Correct term Incorrect terminology
Hemangioma Strawberry Hemangioma

Capillary Hemangioma

Cavernous Hemangioma

Kaposiform hemangioendothelioma (Capillary) Hemangioma
Pyogenic granuloma Hemangioma
Capillary Malformation Port-wine stain

Capillary Hemangioma

Lymphatic Malformation Lymphangioma

Cystic hygroma

Venous Malformation Cavernous Hemangioma
Arteriovenous malformation Arteriovenous Hemangioma


Classification

Vascular tumors
  • Infantile Hemangioma
    • Appears in first 4 weeks of life
    • Grows over 9-12 months
    • Then often involutes
  • Congenital Hemangioma
    • Fully formed at birth
    • Types:
      • Rapidly involuting congenital hemangioma (RICH)
      • Non-involuting congenital hemangioma (NICH)
  • Kaposiform Hemangioendothelioma
    • Locally aggressive but not metastatic
    • => Thrombocytopenia due to sequestration of platelets
    • Hard to treat surgically
    • Use interferon alpha
  • Pyogenic granuloma
    • Small, benign
    • May be complicated by bleeding, crusting and ulceration

Vascular malformations
  • Slow-flow vascular malformations
    • Capillary malformation
      • Flat, reddish lesions that typically affect the skin, mostly around the head and the neck
      • Darken with age
    • Venous malformation
      • Bluish lesion
      • Compressible on palpation
      • Enlarge with physical activity or a dependent position
    • Lymphatic malformation
  • Fast-flow vascular malformations
    • Arterial malformation
    • Arteriovenous fistula (AVF)
    • Arteriovenous malformation
  • Combined-complex vascular malformations
    • CVM: capillary venous malformation
    • CLM: capillary lymphatic malformation
    • LVM: lymphatic venous malformation
    • CLVM: capillary lymphatic venous malformation
    • AVM-LM: Arteriovenous malformation- lymphatic malformation
    • CM-AVM: capillary malformation- arteriovenous malformation


Phakomatoses

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